Cystic fibrosis.
Lancet. 388: 2519-2531Immune responses in cystic fibrosis: are they intrinsically defective?.
Am J Respir Cell Mol Biol. 46: 715-722Tousson A Van Tine BA Naren AP Shaw GM Schwiebert LMCharacterization of CFTR expression and chloride channel activity in human endothelia.
Am J Physiol. 275: C1555-C1564Vizzardi E Sciatti E Bonadei I Cani DS Menotti E Prati F Dallapellegrina L Metra M Berlendis M Poli P Padoan RMacro- and microvascular functions in cystic fibrosis adults without cardiovascular risk factors: A case-control study.
Monaldi Arch Chest Dis. : 89Bano–Rodrigo A Salcedo–Posadas A Villa–Asensi JR Tamariz–Martel A Lopez–Neyra A Blanco–Iglesias ERight ventricular dysfunction in adolescents with mild cystic fibrosis.
J Cyst Fibros. 11: 274-280Bright–Thomas RJ Webb AKThe heart in cystic fibrosis.
J R Soc Med. 95: 2-10Cystic fibrosis complicated by cor pulmonale: the first case report in Taiwan.
Pediatr Neonatol. 59: 310-311Burgel PR Bellis G Olesen HV Viviani L Zolin A Blasi F Elborn JS EETFoPoCfAwCFi EuropeFuture trends in cystic fibrosis demography in 34 European countries.
Eur Respir J. 46: 133-141Heijerman HGM McKone EF Downey DG Van Braeckel E Rowe SM Tullis E Mall MA Welter JJ Ramsey BW McKee CM Marigowda G Moskowitz SM Waltz D Sosnay PR Simard C Ahluwalia N Xuan F Zhang Y Taylor–Cousar JL McCoy KSGroup VXT: Efficacy and safety of the elexacaftor plus tezacaftor plus ivacaftor combination regimen in people with cystic fibrosis homozygous for the F508del mutation: a double-blind, randomised, phase 3 trial.
Lancet. 394: 1940-1948Middleton PG Mall MA Drevinek P Lands LC McKone EF Polineni D Ramsey BW Taylor–Cousar JL Tullis E Vermeulen F Marigowda G McKee CM Moskowitz SM Nair N Savage J Simard C Tian S Waltz D Xuan F Rowe SM Jain R Group VXSElexacaftor–Tezacaftor–Ivacaftor for cystic fibrosis with a single Phe508del Allele.
N Engl J Med. 381: 1809-1819Regard L Lafoeste H Martin C Chassagnon G Burgel PR[Ageing with cystic fibrosis: Classical and emerging comorbidities in adults with cystic fibrosis].
Rev Pneumol Clin. 74: 279-291Nowak JK Szczepanik M Wojsyk–Banaszak I Madry E Wykretowicz A Krzyzanowska–Jankowska P Drzymala–Czyz S Nowicka A Pogorzelski A Sapiejka E Skorupa W Miskiewicz–Chotnicka A Lisowska A Walkowiak JCystic fibrosis dyslipidaemia: a cross–sectional study.
J Cyst Fibros. 18: 566-571Jiang K Jiao S Vitko M Darrah R Flask CA Hodges CA Yu XThe impact of cystic fibrosis transmembrane regulator disruption on cardiac function and stress response.
J Cyst Fibros. 15: 34-42Duan D Ye L Britton F Miller LJ Yamazaki J Horowitz B Hume JRPurinoceptor-coupled Cl- channels in mouse heart: a novel, alternative pathway for CFTR regulation.
J Physiol. 521: 43-56Warth JD Collier ML Hart P Geary Y Gelband CH Chapman T Horowitz B Hume JRCFTR chloride channels in human and simian heart.
Cardiovasc Res. 31: 615-624Sellers ZM Kovacs A Weinheimer CJ Best PMLeft ventricular and aortic dysfunction in cystic fibrosis mice.
J Cyst Fibros. 12: 517-524Sellers ZM McGlocklin L Brasch AStrain rate echocardiography uncovers subclinical left ventricular dysfunction in cystic fibrosis.
J Cyst Fibros. 14: 654-660Eising JB van der Ent CK Teske AJ Vanderschuren MM Uiterwaal C Meijboom FJYoung patients with cystic fibrosis demonstrate subtle alterations of the cardiovascular system.
J Cyst Fibros. Ozcelik N Shell R Holtzlander M Cua CDecreased right ventricular function in healthy pediatric cystic fibrosis patients versus non-cystic fibrosis patients.
Pediatr Cardiol. 34: 159-164Koelling TM Dec GW Ginns LC Semigran MJLeft ventricular diastolic function in patients with advanced cystic fibrosis.
Chest. 123: 1488-1494Labombarda F Saloux E Brouard J Bergot E Milliez PHeart involvement in cystic fibrosis: a specific cystic fibrosis-related myocardial changes?.
Respir Med. 118: 31-38Florea VG Florea ND Sharma R Coats AJ Gibson DG Hodson ME Henein MYRight ventricular dysfunction in adult severe cystic fibrosis.
Chest. 118: 1063-1068De Wolf D Franken P Piepsz A Dab ILeft ventricular perfusion deficit in patients with cystic fibrosis.
Pediatr Pulmonol. 25: 93-98Sullivan MM Moss RB Hindi RD Lewiston NJSupraventricular tachycardia in patients with cystic fibrosis.
Chest. 90: 239-242Florencio R Fregonezi G Brilhante S Borghi–Silva A Dias F Resqueti VHeart rate variability at rest and after the 6–minute walk test (6MWT) in children with cystic fibrosis.
Braz J Phys Ther. 17: 419-426D'Angelo AM Chan EG Hayanga JW Odell DD Pilewski J Crespo M Morrell M Shigemura N Luketich J Bermudez C Althouse AD D'Cunha JAtrial arrhythmias after lung transplantation: incidence and risk factors in 652 lung transplant recipients.
J Thorac Cardiovasc Surg. 152: 901-909See VY Roberts–Thomson KC Stevenson WG Camp PC Koplan BAAtrial arrhythmias after lung transplantation: epidemiology, mechanisms at electrophysiology study, and outcomes.
Circ Arrhythm Electrophysiol. 2: 504-510Avedissian SN Rhodes NJ Ng TMH Rao AP Beringer PMThe potential for qt interval prolongation with chronic azithromycin therapy in adult cystic fibrosis patients.
Pharmacotherapy. 39: 718-723Cardiotoxicity of fluoroquinolones.
J Antimicrob Chemother. 49: 593-596Costantino S Paneni F Cosentino FAgeing, metabolism and cardiovascular disease.
J Physiol. 594: 2061-2073Robert R Savineau JP Norez C Becq F Guibert CExpression and function of cystic fibrosis transmembrane conductance regulator in rat intrapulmonary arteries.
Eur Respir J. 30: 857-864Vizzardi E Sciatti E Bonadei I Menotti E Prati F Scodro M Dallapellegrina L Berlendis M Poli P Padoan R Metra MElastic aortic properties in cystic fibrosis adults without cardiovascular risk factors: a case-control study.
Echocardiography. 36: 1118-1122Zouk AN Gulati S Xing D Wille KM Rowe SM Wells JMPulmonary artery enlargement is associated with pulmonary hypertension and decreased survival in severe cystic fibrosis: a cohort study.
PLoS One. 15e0229173Prognostic significance of pulmonary hypertension in patients with cystic fibrosis: a systematic review and meta-analysis.
Medicine (Baltimore). 97: e9708Pulmonary hypertension survival effects and treatment options in cystic fibrosis.
Curr Opin Pulm Med. 19: 652-661Pulmonary artery hypertension: an underrated disease manifestation in cystic fibrosis?.
Lancet Respir Med. 4: 596-598Galie N Humbert M Vachiery JL Gibbs S Lang I Torbicki A Simonneau G Peacock A Vonk Noordegraaf A Beghetti M Ghofrani A Gomez Sanchez MA Hansmann G Klepetko W Lancellotti P Matucci M McDonagh T Pierard LA Trindade PT Zompatori M 2015 Hoeper M:ESC/ERS guidelines for the diagnosis and treatment of pulmonary hypertension: the joint task force for the diagnosis and treatment of pulmonary hypertension of the european society of cardiology (ESC) and the European respiratory society (ERS): endorsed by: association for european paediatric and congenital cardiology (AEPC), international society for heart and lung transplantation (ISHLT).
Eur Respir J. 46: 903-975Augustine DX Coates–Bradshaw LD Willis J Harkness A Ring L Grapsa J Coghlan G Kaye N Oxborough D Robinson S Sandoval J Rana BS Siva A Nihoyannopoulos P Howard LS Fox K Bhattacharyya S Sharma V Steeds RP Mathew TEchocardiographic assessment of pulmonary hypertension: a guideline protocol from the British Society of Echocardiography.
Echo Res Pract. 5 ()Goldring RM Fishman AP Turino GM Cohen HI Denning CR Andersen DHPulmonary hypertension and cor pulmonale in cystic fibrosis of the pancreas.
J Pediatr. 65: 501-524Sciatti E Vizzardi E Bonadei I Valentini F Menotti E Prati F Dallapellegrina L Berlendis M Poli P Padoan R Metra MFocus on echocardiographic right ventricular strain analysis in cystic fibrosis adults without cardiovascular risk factors: a case-control study.
Intern Emerg Med. 14: 1279-1285Dorfmuller P Perros F Balabanian K Humbert MInflammation in pulmonary arterial hypertension.
Eur Respir J. 22: 358-363Goldenberg NM Steinberg BEInflammation drives pulmonary arterial hypertension.
Anesthesiology. 130: 820-821Hall S Brogan P Haworth SG Klein NContribution of inflammation to the pathology of idiopathic pulmonary arterial hypertension in children.
Thorax. 64: 778-783Lan NSH Massam BD Kulkarni SS Lang CCPulmonary arterial hypertension: pathophysiology and treatment.
Diseases. : 6Elizur A Cannon CL Ferkol TWAirway inflammation in cystic fibrosis.
Chest. 133: 489-495Poore S Berry B Eidson D McKie KT Harris RAEvidence of vascular endothelial dysfunction in young patients with cystic fibrosis.
Chest. 143: 939-945Noe J Petrusca D Rush N Deng P VanDemark M Berdyshev E Gu Y Smith P Schweitzer K Pilewsky J Natarajan V Xu Z Obukhov AG Petrache ICFTR regulation of intracellular pH and ceramides is required for lung endothelial cell apoptosis.
Am J Respir Cell Mol Biol. 41: 314-323Verhaeghe C Tabruyn SP Oury C Bours V Griffioen AWIntrinsic pro–angiogenic status of cystic fibrosis airway epithelial cells.
Biochem Biophys Res Commun. 356: 745-749Wells JM Farris RF Gosdin TA Dransfield MT Wood ME Bell SC Rowe SMPulmonary artery enlargement and cystic fibrosis pulmonary exacerbations: a cohort study.
Lancet Respir Med. 4: 636-645Efrati O Harash O Rivlin J Bibi H Meir MZ Blau H Mussaffi H Barak A Levy I Vilozni D Kerem EModan–Moses D: Hemoptysis in Israeli CF patients–prevalence, treatment, and clinical characteristics.
J Cyst Fibros. 7: 301-306Barben J Robertson D Olinsky A Ditchfield MBronchial artery embolization for hemoptysis in young patients with cystic fibrosis.
Radiology. 224: 124-130Monroe EJ Pierce DB Ingraham CR Johnson GE Shivaram GM Valji KAn interventionalist's guide to hemoptysis in cystic fibrosis.
Radiographics. 38: 624-641Walker CM Rosado–de–Christenson ML Martinez–Jimenez S Kunin JR Wible BCBronchial arteries: anatomy, function, hypertrophy, and anomalies.
Radiographics. 35: 32-49Wand O Guber E Guber A Epstein Shochet G Israeli–Shani L Shitrit DInhaled tranexamic acid for hemoptysis treatment: a randomized controlled trial.
Chest. 154: 1379-1384Cystic Fibrosis FoundationPatient Registry Annual Data Report 2019.
www.cff.org, Bethesda, MDBatra K Chamarthy MR Reddick M Roda MS Wait M Kalva SPDiagnosis and interventions of vascular complications in lung transplant.
Cardiovasc Diagn Ther. 8: 378-386Denton EJ Rischin A McGiffin D Williams TJ Paraskeva MA Westall GP Snell GRefractory pulmonary edema caused by late pulmonary vein thrombosis after lung transplantation: a rare adverse event.
Ann Thorac Surg. 102 ()Miyaji K Nakamura K Maruo T Morita H Saito H Emori T Goto K Date H Ohe TEffect of a kink in unilateral pulmonary artery anastomosis on velocities of blood flow through bilateral pulmonary vein anastomoses in living-donor lobar lung transplantation.
J Am Soc Echocardiogr. 17: 998-999Anaya–Ayala JE Loebe M Davies MGEndovascular management of early lung transplant–related anastomotic pulmonary artery stenosis.
J Vasc Interv Radiol. 26: 878-882Dai DW Garber B Weigt SS Worswick S Kubak BM Lynch 3rd, JP Shino MY DerHovanessian A Saggar R Ross DJ Sayah DMPulmonary allograft versus host disease.
Transplant Direct. 3: e333Cardiovascular toxicities of immunosuppressive agents.
Am J Transplant. 2: 807-818Dogan P Grbovic E Inci S Bayraktar F Cagli KAzathioprine-induced atrial fibrillation.
Intractable Rare Dis Res. 4: 207-209Immunosuppression for lung transplantation.
Proc Am Thorac Soc. 6: 47-53Skolnik K Levy RD Wilcox PG Quon BSCoronary artery disease in cystic fibrosis: An emerging concern?.
J Cyst Fibros. 15 ()Ischaemic heart disease––a new issue in cystic fibrosis?.
J R Soc Med. 103: S44-S48Reverri EJ Morrissey BM Cross CE Steinberg FMInflammation, oxidative stress, and cardiovascular disease risk factors in adults with cystic fibrosis.
Free Radic Biol Med. 76: 261-277Figueroa V Milla C Parks EJ Schwarzenberg SJ Moran AAbnormal lipid concentrations in cystic fibrosis.
Am J Clin Nutr. 75: 1005-1011Rhodes B Nash EF Tullis E Pencharz PB Brotherwood M Dupuis A Stephenson APrevalence of dyslipidemia in adults with cystic fibrosis.
J Cyst Fibros. 9: 24-28Zemanick ET Wagner BD Robertson CE Stevens MJ Szefler SJ Accurso FJ Sagel SD Harris JKAssessment of airway microbiota and inflammation in cystic fibrosis using multiple sampling methods.
Ann Am Thorac Soc. 12: 221-229Hart NJ Aramandla R Poffenberger G Fayolle C Thames AH Bautista A Spigelman AF Babon JAB DeNicola ME Dadi PK Bush WS Balamurugan AN Brissova M Dai C Prasad N Bottino R Jacobson DA Drumm ML Kent SC MacDonald PE Powers ACCystic fibrosis–related diabetes is caused by islet loss and inflammation.
JCI Insight. : 3Gangell C Gard S Douglas T Park J de Klerk N Keil T Brennan S Ranganathan S Robins–Browne R Sly PD Arest CFInflammatory responses to individual microorganisms in the lungs of children with cystic fibrosis.
Clin Infect Dis. 53: 425-432Sagel SD Sontag MK Accurso FJRelationship between antimicrobial proteins and airway inflammation and infection in cystic fibrosis.
Pediatr Pulmonol. 44: 402-409Sagel SD Chmiel JF Konstan MWSputum biomarkers of inflammation in cystic fibrosis lung disease.
Proc Am Thorac Soc. 4: 406-417Inflammation in atherosclerosis.
Arterioscler Thromb Vasc Biol. 32: 2045-2051Sagel SD Thompson V Chmiel JF Montgomery GS Nasr SZ Perkett E Saavedra MT Slovis B Anthony MM Emmett P Heltshe SLEffect of treatment of cystic fibrosis pulmonary exacerbations on systemic inflammation.
Ann Am Thorac Soc. 12: 708-717Bonfield TL Panuska JR Konstan MW Hilliard KA Hilliard JB Ghnaim H Berger MInflammatory cytokines in cystic fibrosis lungs.
Am J Respir Crit Care Med. 152: 2111-2118The role of TNF in cardiovascular disease.
Pharmacol Res. 40: 97-105Greally P Hussein MJ Cook AJ Sampson AP Piper PJ Price JFSputum tumour necrosis factor–alpha and leukotriene concentrations in cystic fibrosis.
Arch Dis Child. 68: 389-392Mitola S Sorbello V Ponte E Copreni E Mascia C Bardessono M Goia M Biasi F Conese M Poli G Bussolino F De Rose VTumor necrosis factor–alpha in airway secretions from cystic fibrosis patients upregulate endothelial adhesion molecules and induce airway epithelial cell apoptosis: implications for cystic fibrosis lung disease.
Int J Immunopathol Pharmacol. 21: 851-865Interleukin–6 and cardiovascular diseases.
Jpn Heart J. 45: 183-193Ordonez CL Henig NR Mayer–Hamblett N Accurso FJ Burns JL Chmiel JF Daines CL Gibson RL McNamara S Retsch–Bogart GZ Zeitlin PL Aitken MLInflammatory and microbiologic markers in induced sputum after intravenous antibiotics in cystic fibrosis.
Am J Respir Crit Care Med. 168: 1471-1475Schumacher SM Naga Prasad SVTumor necrosis factor-alpha in heart failure: an updated review.
Curr Cardiol Rep. 20: 117Hunt WR Helfman BR McCarty NA Hansen JMAdvanced glycation end products are elevated in cystic fibrosis-related diabetes and correlate with worse lung function.
J Cyst Fibros. 15: 681-688Hameed S Jaffe A Verge CFAdvances in the detection and management of cystic fibrosis related diabetes.
Curr Opin Pediatr. 27: 525-533Cystic fibrosis related diabetes.
Curr Diab Rep. 14: 511Olesen HV Drevinek P Gulmans VA Hatziagorou E Jung A Mei–Zahav M Stojnic N Thomas M Zolin A Group ESCystic fibrosis related diabetes in Europe: Prevalence, risk factors and outcome; Olesen et al..
J Cyst Fibros. Granados A Chan CL Ode KL Moheet A Moran A Holl RCystic fibrosis related diabetes: pathophysiology, screening and diagnosis.
J Cyst Fibros. 18 ()Cystic Fibrosis F.
: 1-85Kelly A De Leon DD Sheikh S Camburn D Kubrak C Peleckis AJ Stefanovski D Hadjiliadis D Rickels MR Rubenstein RCIslet Hormone and Incretin Secretion in Cystic Fibrosis after Four Months of Ivacaftor Therapy.
Am J Respir Crit Care Med. 199: 342-351Thomassen JC Mueller MI Alejandre Alcazar MA Rietschel E van Koningsbruggen–Rietschel SEffect of Lumacaftor/Ivacaftor on glucose metabolism and insulin secretion in Phe508del homozygous cystic fibrosis patients.
J Cyst Fibros. 17: 271-275Premature vascular ageing in cystic fibrosis.
Eur Respir J. 34: 1217-1218Rodriguez–Miguelez P Thomas J Seigler N Crandall R McKie KT Forseen C Harris RAEvidence of microvascular dysfunction in patients with cystic fibrosis.
Am J Physiol Heart Circ Physiol. 310: H1479-H1485Cook DP Rector MV Bouzek DC Michalski AS Gansemer ND Reznikov LR Li X Stroik MR Ostedgaard LS Abou Alaiwa MH Thompson MA Prakash YS Krishnan R Meyerholz DK Seow CY Stoltz DACystic fibrosis transmembrane conductance regulator in sarcoplasmic reticulum of airway smooth muscle. Implications for airway contractility.
Am J Respir Crit Care Med. 193: 417-426Hubner CA Schroeder BC Ehmke HRegulation of vascular tone and arterial blood pressure: role of chloride transport in vascular smooth muscle.
Pflugers Arch. 467: 605-614Peters W Kusche–Vihrog K Oberleithner H Schillers HCystic fibrosis transmembrane conductance regulator is involved in polyphenol–induced swelling of the endothelial glycocalyx.
Nanomedicine. 11: 1521-1530Totani L Plebani R Piccoli A Di Silvestre S Lanuti P Recchiuti A Cianci E Dell'Elba G Sacchetti S Patruno S Guarnieri S Mariggio MA Mari VC Anile M Venuta F Del Porto P Moretti P Prioletta M Mucilli F Marchisio M Pandolfi A Evangelista V Romano MMechanisms of endothelial cell dysfunction in cystic fibrosis.
Biochim Biophys Acta. 1863: 3243-3253Hull JH Garrod R Ho TB Knight RK Cockcroft JR Shale DJ Bolton CEIncreased augmentation index in patients with cystic fibrosis.
Eur Respir J. 34: 1322-1328Hull JH Garrod R Ho TB Knight RK Cockcroft JR Shale DJ Bolton CEDynamic vascular changes following intravenous antibiotics in patients with cystic fibrosis.
J Cyst Fibros. 12: 125-129Buehler T Steinmann M Singer F Regamey N Casaulta C Schoeni MH Simonetti GDIncreased arterial stiffness in children with cystic fibrosis.
Eur Respir J. 39: 1536-1537Schwarzenberg SJ Thomas W Olsen TW Grover T Walk D Milla C Moran AMicrovascular complications in cystic fibrosis–related diabetes.
Diabetes Care. 30: 1056-1061Low blood pressure in young adults with cystic fibrosis: an effect of chronic salt loss in sweat?.
Ann Intern Med.
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